Henning J Scott, Witkiewicz Agnieszka, Schaffer Julie V, Orlow Seth J
Department of Dermatology, New York University School of Medicine, USA.
Dermatol Online J. 2005 Dec 30;11(4):11.
A 3-year-old girl presented with a 6-month history of multiple, light-pink, flat-topped papules over the dorsal aspects of the metacarpophalangeal and interphalangeal joints of the hands and feet. Nailfold telangiectases, ragged cuticles, and a heliotrope color of the upper eyelids were also evident, but there was no clinical evidence of muscle weakness and levels of muscle enzymes were normal. A biopsy specimen from one of the papules showed a vacuolar interface dermatitis consistent with a diagnosis of dermatomyositis. This report draws attention to juvenile amyopathic dermatomyositis, which is an uncommon subtype of dermatomyositis with an excellent prognosis.
一名3岁女童，双手和双足的掌指关节及指间关节背侧出现多个浅粉色扁平丘疹，病程6个月。甲褶毛细血管扩张、甲小皮粗糙及上眼睑呈淡紫色也很明显，但无肌无力的临床证据，肌酶水平正常。其中一个丘疹的活检标本显示空泡界面性皮炎，符合皮肌炎的诊断。本报告提请注意青少年无肌病性皮肌炎，这是皮肌炎的一种罕见亚型，预后良好。
