Subramaniam Balachundhar, Soriano Sulpicio G, Michael Scott R, Kussman Barry D
Department of Anesthesiology, Perioperative and Pain Medicine, Children's Hospital Boston, Boston, MA 02115, USA.
Paediatr Anaesth. 2006 Jan;16(1):72-6. doi: 10.1111/j.1460-9592.2005.01598.x.
We report the case of a 11-year-old girl with Moyamoya syndrome, who had undergone staged-repair of tricuspid atresia to a Fontan circulation, scheduled to undergo bilateral pial synangiosis. Surgery for the first hemisphere was complicated by intracranial hemorrhage requiring an emergency craniotomy. The case highlights the importance of understanding Fontan physiology and its interrelationship with the cerebral circulation in the setting of cerebrovascular insufficiency and raised intracranial pressure.
我们报告了一例患有烟雾病综合征的11岁女孩的病例,该女孩曾接受三尖瓣闭锁分期修复术以建立Fontan循环,计划接受双侧软脑膜血管吻合术。第一侧半球手术出现颅内出血并发症,需要紧急开颅手术。该病例凸显了在脑血管功能不全和颅内压升高的情况下,理解Fontan循环生理及其与脑循环相互关系的重要性。