Paula Leila C P de, Zen Vanessa L, Czepielewski Mauro A
Serviço de Endocrinologia, Hospital de Clínicas de Porto Alegre, RS.
Arq Bras Endocrinol Metabol. 2005 Oct;49(5):776-83. doi: 10.1590/s0004-27302005000500018. Epub 2006 Jan 23.
Granulosa-stromal tumors comprise 5 to 8% of all primary ovarian neoplasms. The first clinical manifestation is precocious puberty in most prepuberal patients. We report a case of mixed germ cell-cord stromal tumor of ovary in a 7.2 years old girl, who presented with isosexual pseudo-precocious puberty of progressive outcome. Serum testosterone, estradiol and 17alphaOH-progesterone levels were increased. Abdominal-pelvic ultrasound revealed a right ovarian mass. Unilateral salpingo-oophorectomy was performed with complete resection of the tumor. The patient is well 7 years after surgery with normal pubertal and growth development and no signs of tumor relapse. We review the clinical manifestations of ovarian tumors, classification and staging of sex cord-stromal tumors, follow-up, tumor markers, treatment and prognosis.
颗粒-间质细胞瘤占所有原发性卵巢肿瘤的5%至8%。在大多数青春期前患者中,其首发临床表现为性早熟。我们报告一例7.2岁女孩的卵巢混合性生殖细胞-性索间质肿瘤,该患儿表现为进展性的同性假性性早熟。血清睾酮、雌二醇和17α-羟孕酮水平升高。腹盆腔超声显示右侧卵巢有肿块。行单侧输卵管卵巢切除术,肿瘤完整切除。术后7年,患者情况良好,青春期和生长发育正常,无肿瘤复发迹象。我们回顾了卵巢肿瘤的临床表现、性索间质肿瘤的分类和分期、随访、肿瘤标志物、治疗及预后。