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[白塞病——诊断与治疗难题]

[Behçet's disease--difficulty in diagnostic and management].

作者信息

Swierkot Jerzy, Borysewicz Krzysztof, Szechiński Jacek

机构信息

Zakład Reumatologii AM we Wrocławiu.

出版信息

Pol Arch Med Wewn. 2005 Jun;113(6):580-4.

Abstract

We present a 31-year-old female patient with Behçet's disease. Behcet's disease is a systematic vasculitis of unknown cause involving veins and arteries of all sizes and having reccurent mucocutaneous and frequent ocular involvement. Our patient was suffering from oral and genital ulcers, fever, painful left knee and erythema nodosum. After having excluded differential diagnoses Behçet's disease was diagnosed. The treatment must be individual and it depends on the presence and severity of symptoms. The optimal improvement was observed after treatment with azathioprine, cyclosporine A and metylprednisolon. Behçet's disease is very seldom in our country but perhaps sometimes it isn't good diagnosed.

摘要

我们报告一名31岁的白塞病女性患者。白塞病是一种病因不明的系统性血管炎,累及各种大小的动静脉,常伴有复发性黏膜皮肤病变和眼部受累。我们的患者患有口腔和生殖器溃疡、发热、左膝关节疼痛和结节性红斑。排除鉴别诊断后,诊断为白塞病。治疗必须个体化,取决于症状的存在和严重程度。使用硫唑嘌呤、环孢素A和甲泼尼龙治疗后观察到最佳改善效果。白塞病在我国非常少见,但有时可能诊断不佳。

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