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Late presentation of alveolar capillary dysplasia in an infant.

作者信息

Shankar Venkat, Haque Anwarul, Johnson Joyce, Pietsch John

机构信息

Divisions of Pediatric Critical Care Medicine, Monroe Carell Jr. Children's Hospital at Vanderbilt, Nashville, TN, USA.

出版信息

Pediatr Crit Care Med. 2006 Mar;7(2):177-9. doi: 10.1097/01.PCC.0000202570.58016.67.

DOI:10.1097/01.PCC.0000202570.58016.67
PMID:16474258
Abstract

OBJECTIVE

To report a case of late presentation of alveolar capillary dysplasia and misalignment of pulmonary veins.

DESIGN

Descriptive case report.

SETTING

Pediatric intensive care unit of a tertiary care children's hospital.

PATIENT

Seven-week-old female infant with severe hypoxemic respiratory failure.

CONCLUSION

Alveolar capillary dysplasia with misalignment of pulmonary veins is a cause of primary pulmonary hypertension in newborns that can rarely present past the newborn period. Early lung biopsy can be helpful in establishing the diagnosis and avoiding ineffective, futile, and expensive therapeutic interventions.

摘要

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