De Luca Giuseppe, Zamparelli Marcello, Fadda Carlo, Martone Antonio
Department of Oncology, Santobono-Pausilipon National Children's Hospital, Naples 80129, Italy.
J Pediatr Surg. 2006 Feb;41(2):456-7. doi: 10.1016/j.jpedsurg.2005.11.026.
Focal nodular hyperplasia of the liver is a benign disorder usually affecting young women. Its treatment in children is traditionally conservative. Because of its rarity in childhood, its differential diagnosis with other hepatic tumors in children and infants is challenging. We present the case of a 7-month-old infant with large focal nodular hyperplasia affecting the whole left liver lobe. Because of progressive enlargement of the lesion and compression of the portal vein, the baby underwent successful surgical treatment. Different therapeutic options and relative indications are discussed.
肝脏局灶性结节性增生是一种通常影响年轻女性的良性疾病。传统上,其在儿童中的治疗是保守的。由于其在儿童期罕见,与儿童和婴儿其他肝脏肿瘤的鉴别诊断具有挑战性。我们报告一例7个月大的婴儿,患有累及整个左肝叶的巨大肝脏局灶性结节性增生。由于病变逐渐增大并压迫门静脉,该婴儿接受了成功的手术治疗。文中讨论了不同的治疗选择及相关适应证。