Dikensoy Oner, Kervancioglu Resat, Bayram Nazan Gulhan, Elbek Osman, Uyar Meral, Ekinci Erhan
Department of Pulmonary Diseases, Gaziantep University, Turkey.
J Thorac Imaging. 2006 Mar;21(1):73-5. doi: 10.1097/01.rti.0000203635.36135.0d.
Horseshoe lung is a rare congenital anomaly characterized by the presence of unilateral pulmonary hypoplasia and a midline isthmus bridging the right and the left lung. Almost all cases of horseshoe lung are associated with the scimitar syndrome. The scimitar syndrome, sometimes called the congenital pulmonary venolobar syndrome, is a rare but well-described constellation of cardio-pulmonary anomalies. The characteristic abnormality is anomalous pulmonary venous return from a part of or the entire right lung to the inferior vena cava. We present a case of horseshoe lung associated with scimitar syndrome and pleural lipoma in an adult admitted for acute chest pain and chronic dyspnea.
马蹄肺是一种罕见的先天性异常,其特征为单侧肺发育不全以及连接右肺和左肺的中线峡部。几乎所有马蹄肺病例都与弯刀综合征相关。弯刀综合征,有时称为先天性肺静脉叶综合征,是一种罕见但已得到充分描述的心肺异常组合。其特征性异常是部分或整个右肺的肺静脉异常回流至下腔静脉。我们报告一例成年患者,因急性胸痛和慢性呼吸困难入院,诊断为马蹄肺合并弯刀综合征及胸膜脂肪瘤。