Vassallo M, Pascotto M, Pisacane C, Santoro G, Paladini D, Russo M G, Calabrò R
Fetal Cardiology Unit, Department of Obstetrics and Gynecology, University Federico II of Naples, Italy.
Ultrasound Obstet Gynecol. 2006 Apr;27(4):445-8. doi: 10.1002/uog.2758.
Right superior vena cava (RSVC) draining into the left atrium, causing hypoxemia, represents a very rare congenital malformation which has not previously been described in the fetus. We describe a case in which fetal echocardiography at 22 weeks' gestation revealed an enlarged superior vena cava connecting abnormally with a mildly enlarged left atrium. Neonatal transthoracic echocardiography confirmed the diagnosis and showed an abnormal connection of the right pulmonary veins to the RSVC. Right-to-left shunt due to anomalous drainage of the RSVC into the left atrium associated with an atrial septal defect and anomalous pulmonary venous return were diagnosed on echocardiography and confirmed by angiography. The newborn was hemodynamically stable at birth and at the 1-year follow-up.
右上腔静脉（RSVC）引流至左心房，导致低氧血症，这是一种非常罕见的先天性畸形，此前尚未在胎儿中描述过。我们描述了一例病例，妊娠22周时的胎儿超声心动图显示上腔静脉扩大，与轻度扩大的左心房异常相连。新生儿经胸超声心动图证实了诊断，并显示右肺静脉与右上腔静脉异常连接。超声心动图诊断为右上腔静脉异常引流至左心房导致的右向左分流，伴有房间隔缺损和肺静脉异常回流，并经血管造影证实。新生儿出生时及1年随访时血流动力学稳定。
