Carmack Adrienne J K, Castellan Miguel, Perez-Brayfield Marcos, Gosalbez Rafael
Department of Urology, University of Miami, Miami, FL 33101, USA.
J Pediatr Surg. 2006 Apr;41(4):e1-3. doi: 10.1016/j.jpedsurg.2006.01.056.
A 2-month-old child presented for evaluation of prenatal hydronephrosis. Imaging studies were consistent with a right duplex system with a dysplastic, nonfunctioning upper pole and lower pole ureteropelvic junction obstruction. We proceeded with removal of the upper pole and pyeloplasty and were surprised to find a single collecting system with a cystic, dysplastic upper pole segment and the absence of an upper pole pelvis or ureter. The rare diagnosis of a segmental multicystic dysplastic kidney with ipsilateral ureteropelvic junction obstruction was made. We present a review of the case and of previous literature on this topic.
一名2个月大的儿童因产前肾积水前来评估。影像学检查结果与右侧重复肾系统相符，上极发育不良且无功能，下极肾盂输尿管连接部梗阻。我们进行了上极切除术和肾盂成形术，结果惊讶地发现是一个单一的集合系统，有一个囊性、发育不良的上极节段，且没有上极肾盂或输尿管。最终诊断为罕见的节段性多囊性发育不良肾合并同侧肾盂输尿管连接部梗阻。我们在此对该病例及此前关于此主题的文献进行综述。
