表现为继发性假瘤综合征的神经白塞病：病例报告

Neuro-Behçet disease presenting as secondary pseudotumor syndrome: case report.

作者信息

Can Emrah, Kara Bülent, Somer Ayper, Keser Melike, Salman Nuran, Yalçin Işik

机构信息

Istanbul University, Faculty of medicine, Istanbul, Turkey.

出版信息

Eur J Paediatr Neurol. 2006 Mar;10(2):97-9. doi: 10.1016/j.ejpn.2006.02.003. Epub 2006 Apr 3.

DOI:10.1016/j.ejpn.2006.02.003

PMID:16595183

Abstract

Behçet's disease is a multisystemic, recurrent, inflammatory disorder, which has a three-symptom complex comprising uveitis, oral aphtae and genital ulcerations. It is rare in childhood. The prevalence of neurologic involvement in BD is range of 10-49%, and shows a wide spectrum from isolated headache to subacute encephalopathy and severe psychosis. We report a 12-year-old Behçet's disease patient with secondary pseudotumor syndrome due to cerebral vein thrombosis and aim to review the literature.

摘要

白塞病是一种多系统、复发性炎症性疾病，具有由葡萄膜炎、口腔溃疡和生殖器溃疡组成的三联征。在儿童期较为罕见。白塞病神经系统受累的患病率为10%-49%，表现范围广泛，从孤立性头痛到亚急性脑病和严重精神病。我们报告一例12岁因脑静脉血栓形成继发假性肿瘤综合征的白塞病患者，并旨在复习相关文献。