Kiernan Thomas J, Fahy Gerry
Int J Cardiol. 2007 Jan 18;114(3):412-3. doi: 10.1016/j.ijcard.2005.11.090. Epub 2006 Apr 17.
Ebstein's anomaly is a rare congenital cardiac disease initially described by Wilhelm Ebstein in 1866. The primary pathology involves significant apical displacement of the septal tricuspid valve leaflet and the presence of a redundant, elongated, anterior tricuspid valve leaflet. This congenital malformation has multiple known associated morphological and electrophysiological cardiac pathologies. In the present article, we report, to the best of our knowledge for the first time in the literature, a case of Ebstein's anomaly with multiple accessory bypass tracts, dual AV nodal physiology, non-compacted left ventricular myocardium and a patent foramen ovale. Indeed, complete evaluation of the left heart is required in cases of Ebstein's anomaly to accurately assess left ventricular myocardial structure.
埃布斯坦畸形是一种罕见的先天性心脏病,最初由威廉·埃布斯坦于1866年描述。主要病理改变包括隔侧三尖瓣叶显著向心尖移位,以及存在多余、冗长的前叶三尖瓣叶。这种先天性畸形有多种已知的相关心脏形态学和电生理病理学改变。在本文中,据我们所知,我们首次在文献中报道了一例伴有多条附加旁路传导束、双房室结生理功能、左心室心肌致密化不全和卵圆孔未闭的埃布斯坦畸形病例。事实上,对于埃布斯坦畸形病例,需要对左心进行全面评估,以准确评估左心室心肌结构。