Hernández J C, Alfonso C, González L, Samada M, Ramos L, Cepero-Valdez M, Antonio Abdo A, Gómez F, Castellanos R, López O, Ugarte J C, Jordán J
Transplant Service, CIMEQ's Hospital, Havana, Cuba.
J Clin Pathol. 2006 May;59(5):542-5. doi: 10.1136/jcp.2004.024398.
Mesenchymal hamartoma of the liver (MHL) is an uncommon tumour composed of architecturally abnormal bile ducts in an uncommitted myxoid stroma. Most MHL are diagnosed in childhood and few cases have been reported in adults. This report describes a case of a well defined solid mass in the right lobe of the liver in a 51 year old man. Preoperative radiological examination revealed a large completely solid mass. Biopsy showed a dense fibrous stroma with hyalinisation and some bile ducts. A provisional diagnosis of MHL was made. Surgical excision was impossible and liver transplantation was undertaken. Definitive pathology confirmed the diagnosis. Review of published reports shows this to be the fourth case of MHL treated by liver transplantation.
肝间叶性错构瘤（MHL）是一种罕见肿瘤，由未分化黏液样基质中结构异常的胆管组成。大多数MHL在儿童期被诊断出来，成人病例报道较少。本报告描述了一名51岁男性肝脏右叶有一个边界清晰的实性肿块的病例。术前影像学检查显示一个巨大的完全实性肿块。活检显示有玻璃样变的致密纤维基质和一些胆管。初步诊断为MHL。由于无法进行手术切除，遂进行了肝移植。最终病理确诊。对已发表报告的回顾显示，这是第四例接受肝移植治疗的MHL病例。
