Pippi-Salle Joao L, Langer Jacob, Favorito Luciano A
Department of Urology, Hospital for Sick Children, University of Toronto, Toronto, Canada.
Int Braz J Urol. 2006 Mar-Apr;32(2):208-10. doi: 10.1590/s1677-55382006000200014.
This study considers a unilateral renal agenesia associated with agenesia of the epididymis body and tail and the vas deferens and non-palpable left testicle in a 20-month-year-old patient. During laparoscopic procedure, the testicle was positioned at approximately 5 cm above the inguinal ring. The size was appropriate for the age and the head of the epididymis was situated in its normal position. The decision was made to perform the first step of the Fowler-Stephens' surgery and the patient presented a good evolution. The association of male duct system agenesia with unilateral renal agenesia in a patient with cryptorchidism diagnosed by laparoscopy is an extremely rare event, however generally in these cases the testicle is of normal size, presents unaltered hormonal function, and must be preserved.
本研究探讨了一名20个月大患者，其单侧肾缺如并伴有附睾体尾部及输精管缺如，左侧睾丸不可触及。在腹腔镜手术过程中，睾丸位于腹股沟环上方约5厘米处。其大小与年龄相符，附睾头部位于正常位置。决定进行福勒-斯蒂芬斯手术的第一步，患者术后恢复良好。腹腔镜诊断为隐睾症的患者中，男性生殖管道系统缺如与单侧肾缺如相关联的情况极为罕见，然而在这些病例中，睾丸通常大小正常，激素功能未改变，必须予以保留。
