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THE CHEMICAL COMPOSITION OF VOLUNTARY MUSCLE IN MUSCLE DISEASE: A COMPARISON OF PROGRESSIVE MUSCULAR DYSTROPHY WITH OTHER DISEASES TOGETHER WITH A STUDY OF EFFECTS OF GLYCINE AND CREATINE THERAPY.肌肉疾病中随意肌的化学成分:进行性肌营养不良与其他疾病的比较以及甘氨酸和肌酸治疗效果的研究
J Clin Invest. 1938 Jul;17(4):377-83. doi: 10.1172/JCI100963.
2
Origin of urinary creatine in progressive muscular dystrophy.进行性肌营养不良中尿肌酸的来源。
Metabolism. 1952 Jan;1(1):13-9.
3
Drug treatment for facioscapulohumeral muscular dystrophy.面肩肱型肌营养不良症的药物治疗
Cochrane Database Syst Rev. 2004;2004(2):CD002276. doi: 10.1002/14651858.CD002276.pub2.
4
An examination of some factors influencing creatine kinase in the blood of patients with muscular dystrophy.对影响肌营养不良症患者血液中肌酸激酶的一些因素的研究。
Muscle Nerve. 1987 Jan;10(1):15-21. doi: 10.1002/mus.880100105.
5
Isoenzyme distribution of creatine kinase and lactate dehydrogenase in serum and skeletal muscle in Duchenne muscular dystrophy, collagen disease, and other muscular disorders.杜兴氏肌营养不良症、胶原病及其他肌肉疾病患者血清和骨骼肌中肌酸激酶和乳酸脱氢酶的同工酶分布
Clin Chem. 1978 Nov;24(11):1985-9.
6
Treatment with human immunoglobulin G improves the early disease course in a mouse model of Duchenne muscular dystrophy.用人免疫球蛋白G治疗可改善杜氏肌营养不良小鼠模型的早期病程。
J Neurochem. 2016 Jan;136(2):351-62. doi: 10.1111/jnc.13269. Epub 2015 Aug 28.
7
Natural History of Serum Enzyme Levels in Duchenne Muscular Dystrophy and Implications for Clinical Practice.杜氏肌营养不良症患者血清酶水平的自然史及其对临床实践的影响。
Am J Phys Med Rehabil. 2020 Dec;99(12):1121-1128. doi: 10.1097/PHM.0000000000001500.
8
CINRG randomized controlled trial of creatine and glutamine in Duchenne muscular dystrophy.CINRG关于肌酸和谷氨酰胺治疗杜氏肌营养不良症的随机对照试验。
Ann Neurol. 2005 Jul;58(1):151-5. doi: 10.1002/ana.20523.
9
[A clinical trial of creatine monohydrate in muscular dystrophy patients].[肌酸单水合物在肌营养不良患者中的临床试验]
Rinsho Shinkeigaku. 2004 Oct;44(10):661-6.
10
Muscular dystrophy of mink: a new animal model.水貂肌肉萎缩症:一种新的动物模型。
Fed Proc. 1976 Apr;35(5):1218-24.

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1
Cardio-respiratory and phenotypic rescue of dystrophin/utrophin-deficient mice by combination therapy.联合治疗对肌营养不良蛋白/乌司他丁缺陷小鼠的心肺和表型的挽救作用。
EMBO Rep. 2022 Jun 7;23(6):e53955. doi: 10.15252/embr.202153955. Epub 2022 Apr 8.
2
Glycine Enhances Satellite Cell Proliferation, Cell Transplantation, and Oligonucleotide Efficacy in Dystrophic Muscle.甘氨酸增强营养不良肌肉中的卫星细胞增殖、细胞移植和寡核苷酸疗效。
Mol Ther. 2020 May 6;28(5):1339-1358. doi: 10.1016/j.ymthe.2020.03.003. Epub 2020 Mar 10.
3
Myasthenia Gravis.重症肌无力
Can Med Assoc J. 1943 Jun;48(6):510-4.
4
STUDIES ON AMINO ACID METABOLISM. II. BLOOD GLYCINE AND TOTAL AMINO ACIDS IN VARIOUS PATHOLOGICAL CONDITIONS, WITH OBSERVATIONS ON THE EFFECTS OF INTRAVENOUSLY ADMINISTERED GLYCINE.氨基酸代谢研究。II. 各种病理状况下的血液甘氨酸和总氨基酸,并观察静脉注射甘氨酸的效果。
J Clin Invest. 1948 Sep;27(5):655-64. doi: 10.1172/JCI102013.
5
EFFECTS OF THYROID ON CREATINE METABOLISM WITH A DISCUSSION OF THE MECHANISM OF STORAGE AND EXCRETION OF CREATINE BODIES.甲状腺对肌酸代谢的影响,并对肌酸物质的储存及排泄机制进行讨论。
J Clin Invest. 1946 May;25(3):360-77. doi: 10.1172/JCI101717.
6
[Enzyme activity determinations in healthy human musculature and in myopathies. II. Enzyme activity changes in muscle in progressive muscular dystrophy].[健康人体肌肉组织及肌病中的酶活性测定。II. 进行性肌营养不良症中肌肉的酶活性变化]
Klin Wochenschr. 1963 May 15;41:500-9. doi: 10.1007/BF01490019.
7
[Histochemical and biochemical findings in dystrophic myopathy].[营养不良性肌病的组织化学和生化研究结果]
Dtsch Z Nervenheilkd. 1955;173(5-6):503-16.
8
Inorganic phosphate response to intravenous glucose administration in progressive muscular dystrophy.进行性肌营养不良患者静脉注射葡萄糖后无机磷酸盐的反应
J Clin Invest. 1953 Nov;32(11):1061-4. doi: 10.1172/JCI102827.
9
[Muscle energy metabolism in children with progressive muscular dystrophy type Duchenne. Metabolites of the Embden-Meyerhof pathway, the citric acid cycle and high energy phosphates and enzyme activity of alpha-glycerol-oxidase, succinate-dehydrogenase and 6-phospho-gluconate-dehydrogenase (author's transl)].杜兴氏进行性肌营养不良症患儿的肌肉能量代谢。糖酵解途径、柠檬酸循环的代谢产物及高能磷酸盐,以及α-甘油氧化酶、琥珀酸脱氢酶和6-磷酸葡萄糖酸脱氢酶的酶活性(作者译)
Klin Wochenschr. 1973 Oct 1;51(19):957-68. doi: 10.1007/BF01468251.

本文引用的文献

1
A method of estimating phosphagen and some other phosphorus compounds in muscle tissue.一种估算肌肉组织中磷酸肌酸及其他一些磷化合物的方法。
J Physiol. 1929 Oct 23;68(2):193-211. doi: 10.1113/jphysiol.1929.sp002607.
2
Colour Standards for use in the Determination of Iminazoles.用于咪唑测定的颜色标准。
Biochem J. 1925;19(1):42-6. doi: 10.1042/bj0190042.

THE CHEMICAL COMPOSITION OF VOLUNTARY MUSCLE IN MUSCLE DISEASE: A COMPARISON OF PROGRESSIVE MUSCULAR DYSTROPHY WITH OTHER DISEASES TOGETHER WITH A STUDY OF EFFECTS OF GLYCINE AND CREATINE THERAPY.

作者信息

Reinhold J G, Kingsley G R

机构信息

Division of Biochemistry, The Laboratories, Philadelphia General Hospital, Philadelphia.

出版信息

J Clin Invest. 1938 Jul;17(4):377-83. doi: 10.1172/JCI100963.

DOI:10.1172/JCI100963
PMID:16694583
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC434792/
Abstract
摘要