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THE COAGULATION DEFECT IN HEMOPHILIA: THE EFFECT, IN HEMOPHILIA, OF THE PARENTERAL ADMINISTRATION OF A FRACTION OF THE PLASMA GLOBULINS RICH IN FIBRINOGEN.

作者信息

Minot G R, Davidson C S, Lewis J H, Tagnon H J, Taylor F H

机构信息

Thorndike Memorial Laboratory, Second and Fourth Medical Services (Harvard), Boston City Hospital, Boston.

出版信息

J Clin Invest. 1945 Sep;24(5):704-7. doi: 10.1172/JCI101654.

DOI:10.1172/JCI101654
PMID:16695264
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC435506/
Abstract
摘要

相似文献

1
THE COAGULATION DEFECT IN HEMOPHILIA: THE EFFECT, IN HEMOPHILIA, OF THE PARENTERAL ADMINISTRATION OF A FRACTION OF THE PLASMA GLOBULINS RICH IN FIBRINOGEN.血友病中的凝血缺陷:血友病患者注射富含纤维蛋白原的血浆球蛋白组分的效果。
J Clin Invest. 1945 Sep;24(5):704-7. doi: 10.1172/JCI101654.
2
Chemical, clinical and immunological studies on the products of human plasma fractionation; the coagulation defect in hemophilia; the effect in vitro and in vivo on the coagulation time in hemophilia of a prothrombin and fibrinogen-free normal plasma and its derived protein fractions.人血浆成分制品的化学、临床及免疫学研究;血友病的凝血缺陷;无凝血酶原和纤维蛋白原的正常血浆及其衍生蛋白组分对血友病患者体内外凝血时间的影响。
J Clin Invest. 1946 Nov;25(6):876-9.
3
The relation of certain fractions of the plasma globulins to the coagulation defect in hemophilia.血浆球蛋白的某些组分与血友病凝血缺陷的关系。
Blood. 1946 Mar;1:166-72.
4
CHEMICAL, CLINICAL AND IMMUNOLOGICAL STUDIES ON THE PRODUCTS OF HUMAN PLASMA FRACTIONATION. XXXIII. THE COAGULATION DEFECT IN HEMOPHILIA: THE EFFECT IN VITRO AND IN VIVO ON THE COAGULATION TIME IN HEMOPHILIA OF A PROTHROMBIN AND FIBRINOGEN-FREE NORMAL PLASMA AND ITS DERIVED PROTEIN FRACTIONS.人血浆成分制品的化学、临床及免疫学研究。三十三。血友病的凝血缺陷:无凝血酶原和纤维蛋白原的正常血浆及其衍生蛋白组分对血友病患者体外和体内凝血时间的影响。
J Clin Invest. 1946 Nov;25(6):876-9. doi: 10.1172/JCI101775.
5
Fibrinogenolytic demonstration of activation and inhibition of tryptase in plasma protein fraction-I (antihemophilic globulin).血浆蛋白组分I(抗血友病球蛋白)中凝血酶原酶激活和抑制的纤维蛋白原溶解演示。
Proc Soc Exp Biol Med. 1947 Mar;64(3):285-9. doi: 10.3181/00379727-64-15771.
6
[HEMOSTATIC TRANSFUSION PREPARATIONS PREPARED FROM DONOR BLOOD (ANTIHEMOPHILIC PLASMA, ANTIHEMOPHILIC GLOBULIN, FIBRINOGEN)].[由供血者血液制备的止血输血制剂(抗血友病血浆、抗血友病球蛋白、纤维蛋白原)]
Probl Gematol Pereliv Krovi. 1963 Jun;8:3-9.
7
Chemical, clinical and immunological studies on the products of human plasma fractionation; the coagulation defect in hemophilia; an in vitro and in vivo comparison of normal and hemophilic whole blood, plasma and derived plasma protein fractions.人血浆分馏产物的化学、临床及免疫学研究;血友病中的凝血缺陷;正常及血友病全血、血浆和衍生血浆蛋白组分的体外及体内比较。
J Clin Invest. 1946 Nov;25(6):870-5.
8
[Preparation of a human plasmatic fraction rich in factor VIII (antihemophilic A) and poor in fibrinogen].富含凝血因子VIII(抗血友病因子A)且纤维蛋白原含量低的人血浆组分的制备
Nouv Rev Fr Hematol. 1961 Nov-Dec;1:880-6.
9
THE COAGULATION DEFECT IN HEMOPHILIA: THE CLOT PROMOTING ACTIVITY IN HEMOPHILIA OF BERKEFELDED NORMAL HUMAN PLASMA FREE FROM FIBRINOGEN AND PROTHROMBIN.血友病中的凝血缺陷:不含纤维蛋白原和凝血酶原的伯克费尔德正常人血浆在血友病中的促凝活性。
J Clin Invest. 1939 Sep;18(5):603-8. doi: 10.1172/JCI101074.
10
[Treatment of hemophilia A with Blombaeck and Blombaeck plasma fraction I-O].用布隆贝克和布隆贝克血浆组分I-O治疗甲型血友病
Thromb Diath Haemorrh. 1962;6(Suppl 2):67-72.

引用本文的文献

1
Chemical, physiological, and immunological properties and clinical uses of blood derivatives.血液衍生物的化学、生理和免疫学特性及临床应用。
Experientia. 1947 Apr 15;3(4):125-36. doi: 10.1007/BF02137457.
2
The Management of Blood Preservation and Blood Substitutes.血液保存与血液替代品的管理
Bull N Y Acad Med. 1946 Sep;22(9):451-64.
3
Plasma protein fractions.血浆蛋白组分
Proc R Soc Med. 1948 Apr;41(4):217-24. doi: 10.1177/003591574804100406.
4
Normal and Abnormal Blood Coagulation: A Review.正常与异常血液凝固:综述
J Clin Pathol. 1948 May;1(3):113-43. doi: 10.1136/jcp.1.3.113.
5
STUDIES OF HEMOPHILIA. II. THE ASSAY OF THE ANTIHEMOPHILIC CLOT-PROMOTING PRINCIPLE IN NORMAL HUMAN PLASMA WITH SOME OBSERVATIONS ON THE RELATIVE POTENCY OF CERTAIN PLASMA FRACTIONS.血友病研究。II. 正常人血浆中抗血友病促凝因子的测定及对某些血浆组分相对效力的一些观察。
J Clin Invest. 1948 Jan;27(1):98-105. doi: 10.1172/JCI101929.
6
CHEMICAL, CLINICAL AND IMMUNOLOGICAL STUDIES ON THE PRODUCTS OF HUMAN PLASMA FRACTIONATION. XXXIII. THE COAGULATION DEFECT IN HEMOPHILIA: THE EFFECT IN VITRO AND IN VIVO ON THE COAGULATION TIME IN HEMOPHILIA OF A PROTHROMBIN AND FIBRINOGEN-FREE NORMAL PLASMA AND ITS DERIVED PROTEIN FRACTIONS.人血浆成分制品的化学、临床及免疫学研究。三十三。血友病的凝血缺陷:无凝血酶原和纤维蛋白原的正常血浆及其衍生蛋白组分对血友病患者体外和体内凝血时间的影响。
J Clin Invest. 1946 Nov;25(6):876-9. doi: 10.1172/JCI101775.
7
CHEMICAL, CLINICAL AND IMMUNOLOGICAL STUDIES ON THE PRODUCTS OF HUMAN PLASMA FRACTIONATION: XXXII. THE COAGULATION DEFECT IN HEMOPHILIA. AN IN VITRO AND IN VIVO COMPARISON OF NORMAL AND HEMOPHILIC WHOLE BLOOD, PLASMA AND DERIVED PLASMA PROTEIN FRACTIONS.人血浆成分制品的化学、临床及免疫学研究:XXXII. 血友病中的凝血缺陷。正常与血友病全血、血浆及衍生血浆蛋白组分的体外和体内比较。
J Clin Invest. 1946 Nov;25(6):870-5. doi: 10.1172/JCI101774.
8
Clinical implications of plasma fractionation.血浆分离的临床意义。
Bull N Y Acad Med. 1954 Oct;30(10):735-49.

本文引用的文献

1
STUDIES IN BLOOD COAGULATION: THE COAGULATION PROPERTIES OF CERTAIN GLOBULIN FRACTIONS OF NORMAL HUMAN PLASMA IN VITRO.血液凝固研究:正常人血浆某些球蛋白组分在体外的凝固特性
J Clin Invest. 1945 Sep;24(5):698-703. doi: 10.1172/JCI101653.
2
CHEMICAL, CLINICAL, AND IMMUNOLOGICAL STUDIES ON THE PRODUCTS OF HUMAN PLASMA FRACTIONATION. I. THE CHARACTERIZATION OF THE PROTEIN FRACTIONS OF HUMAN PLASMA.人血浆成分制品的化学、临床及免疫学研究。I. 人血浆蛋白组分的特性
J Clin Invest. 1944 Jul;23(4):417-32. doi: 10.1172/JCI101508.
3
THE COAGULATION DEFECT IN HEMOPHILIA: STUDIES OF THE CLOT PROMOTING ACTIVITY ASSOCIATED WITH PLASMA EUGLOBULIN IN HEMOPHILIA.血友病中的凝血缺陷:血友病患者血浆优球蛋白相关促凝活性的研究
J Clin Invest. 1939 Nov;18(6):821-5. doi: 10.1172/JCI101099.
4
THE COAGULATION DEFECT IN HEMOPHILIA: THE CLOT PROMOTING ACTIVITY IN HEMOPHILIA OF BERKEFELDED NORMAL HUMAN PLASMA FREE FROM FIBRINOGEN AND PROTHROMBIN.血友病中的凝血缺陷:不含纤维蛋白原和凝血酶原的伯克费尔德正常人血浆在血友病中的促凝活性。
J Clin Invest. 1939 Sep;18(5):603-8. doi: 10.1172/JCI101074.
5
THE COAGULATION DEFECT IN HEMOPHILIA. THE EFFECT IN HEMOPHILIA OF INTRAMUSCULAR ADMINISTRATION. OF A GLOBULIN SUBSTANCE DERIVED FROM NORMAL HUMAN PLASMA.血友病中的凝血缺陷。正常人血浆来源的球蛋白物质肌肉注射对血友病的影响。
J Clin Invest. 1937 Sep;16(5):741-7. doi: 10.1172/JCI100899.
6
HEMOPHILIA. II. SOME PROPERTIES OF A SUBSTANCE OBTAINED FROM NORMAL HUMAN PLASMA EFFECTIVE IN ACCELERATING THE COAGULATION OF HEMOPHILIC BLOOD.血友病。二、从正常人血浆中提取的一种物质的某些特性,该物质能有效加速血友病患者血液的凝固。
J Clin Invest. 1937 Jan;16(1):113-24. doi: 10.1172/JCI100829.