Van Geluwe Filiep, Dymarkowski Steven, Crevits Ilse, De Wever Walter, Bogaert Jan
Department of Radiology, University Hospital Gasthuisberg, Herestraat 49, 3000, Leuven, Belgium.
Eur Radiol. 2006 Oct;16(10):2358-65. doi: 10.1007/s00330-006-0249-7. Epub 2006 May 16.
Since the incidence of amyloidosis is increasing, the purpose of this article is to review the imaging features of intrathoracic amyloidosis. Amyloidosis forms a heterogeneous group of disorders characterised by the extracellular deposition of a homologous protein complex. The heart is the most commonly involved organ in the chest. Respiratory amyloidal deposition is much less common and may be generalised, when it occurs as a part of a systemic disease, or it may be restricted only to the respiratory system. Although, the abnormalities are considered non-specific, recent literature suggests-especially for cardiac amyloidosis-specific patterns of abnormalities.
由于淀粉样变性的发病率正在上升，本文旨在综述胸内淀粉样变性的影像学特征。淀粉样变性是一组异质性疾病，其特征是同源蛋白质复合物在细胞外沉积。心脏是胸部最常受累的器官。呼吸道淀粉样沉积则少见得多，当它作为全身性疾病的一部分出现时可能是全身性的，或者可能仅局限于呼吸系统。虽然这些异常被认为是非特异性的，但最近的文献表明，尤其是对于心脏淀粉样变性，存在特定的异常模式。
