[假性肿瘤性神经白塞病]
[Pseudo-tumoral neuro-Behçet's disease].
作者信息
Darmoul M, Habib Bouhaouala M, Smida H, Hedi Dougui M
机构信息
Unité de Neurochirurgie, Hôpital des FSI, La Marsa, Tunisie.
出版信息
Rev Neurol (Paris). 2006 May;162(5):643-7. doi: 10.1016/s0035-3787(06)75060-3.
INTRODUCTION
Clinical involvement of the central nervous system occurs in about 10 to 30 percent of patients with Behçet's disease. Neurological pseudo tumoral presentation is rare.
CASE REPORT
We report a case of pseudo tumoral neuro-Behçet disease in a 38-year-old man, with past history of facial and dorsal folliculitis, who presented suddenly headache, right hemiplegia, aphasia and disturbed consciousness. Neuroradiological investigations showed a pseudo tumoral lesion in the left capsulo-thalamic region extending to the homolateral peduncle. The patient improved with steroid and immunosuppresseur therapy.
CONCLUSION
The clinical and radiological presentation of neuro-Behçet's disease can mimic a brain tumor.
引言
白塞病患者中约10%至30%会出现中枢神经系统受累。神经系统假瘤样表现较为罕见。
病例报告
我们报告一例38岁男性的假瘤样神经白塞病病例，该患者既往有面部和背部毛囊炎病史，突然出现头痛、右侧偏瘫、失语和意识障碍。神经放射学检查显示左侧丘脑-豆状核区有一个假瘤样病变，延伸至同侧脑桥。患者经类固醇和免疫抑制剂治疗后病情好转。
结论
神经白塞病的临床和放射学表现可模仿脑肿瘤。
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