Vignes S, Vidailhet M, Dormont D, Soulié J, Wechsler B
Service de médecine interne, hôpital de la Pitié-Salpétrière, Paris.
Rev Med Interne. 1998 Jan;19(1):55-9. doi: 10.1016/s0248-8663(97)83701-0.
Neurological involvement occurs in 10 to 28% of patients with Behçet's disease.
We report a case of neurological pseudotumoral presentation of Behçet's in a patient with a long standing disease treated with low dose of prednisone and colchicine (1 mg/day), 2 months after withdrawal of colchicine.
Neurological manifestations during Behçet disease can be secondary to direct central nervous system involvement (encephalitis, encephalomyelitis) or vascular angitis (essentially cerebral venous thrombosis and, rarely, intracranial aneurysms). Neurological pseudotumoral presentation is rarely reported.
白塞病患者中10%至28%会出现神经受累情况。
我们报告一例长期患病的白塞病患者出现神经假瘤样表现的病例，该患者一直使用低剂量泼尼松和秋水仙碱（1毫克/天）治疗，在停用秋水仙碱2个月后发病。
白塞病期间的神经表现可能继发于中枢神经系统直接受累（脑炎、脑脊髓炎）或血管性血管炎（主要是脑静脉血栓形成，颅内动脉瘤罕见）。神经假瘤样表现鲜有报道。
