海绵状脑病的新生物学：具有基因变异的传染性淀粉样变性病 - Suppr

The new biology of spongiform encephalopathy: infectious amyloidoses with a genetic twist.

作者信息

Brown P, Goldfarb L G, Gajdusek D C

机构信息

Laboratory of CNS Studies, National Institute of Neurological Disorders and Stroke National Institutes of Health, Bethesda, Maryland 20892.

出版信息

Lancet. 1991 Apr 27;337(8748):1019-22. doi: 10.1016/0140-6736(91)92670-w.

DOI:10.1016/0140-6736(91)92670-w

PMID:1673176

Abstract

摘要

相似文献

The new biology of spongiform encephalopathy: infectious amyloidoses with a genetic twist.海绵状脑病的新生物学：具有基因变异的传染性淀粉样变性病

Lancet. 1991 Apr 27;337(8748):1019-22. doi: 10.1016/0140-6736(91)92670-w.

Genetics of response to slow virus (prion) infection.对慢病毒（朊病毒）感染反应的遗传学

Annu Rev Genet. 1990;24:115-32. doi: 10.1146/annurev.ge.24.120190.000555.

Transthyretin amyloidoses of familial amyloidotic polyneuropathy as a paradigm for the genetic control of spontaneous generation of infectious amyloids by patterned configurational change in host precursors in Creutzfeldt-Jacob disease.家族性淀粉样多神经病的转甲状腺素蛋白淀粉样变性作为克雅氏病中宿主前体通过模式化构型变化自发产生感染性淀粉样蛋白的遗传控制范例。

Acta Med Port. 1991 Dec;4 Suppl 1:9S-15S.

New mutation in scrapie amyloid precursor gene (at codon 178) in Finnish Creutzfeldt-Jakob kindred.芬兰克雅氏病家族中羊瘙痒病淀粉样前体蛋白基因（密码子178处）的新突变

Lancet. 1991 Feb 16;337(8738):425. doi: 10.1016/0140-6736(91)91198-4.

Prion dementia without characteristic pathology.无特征性病理学改变的朊病毒痴呆症

Lancet. 1990 Jul 7;336(8706):7-9. doi: 10.1016/0140-6736(90)91518-f.

[Conjugal form of subacute spongy encephalopathy. (Jakob-Creutzfeldt disease)].[亚急性海绵状脑病的婚姻形式。（雅各布 - 克雅氏病）]

Wien Klin Wochenschr. 1972 Apr 14;84(15):245-9.

[The clinical syndrome of presenile idiopathic encephalopathy ("Jakob-Creutzfeldt-syndrome") or spongiform encephalopathy (author's transl)].

Arch Psychiatr Nervenkr (1970). 1973 Nov 27;218(1):1-40. doi: 10.1007/BF00347086.

Experimental transmission of an autosomal dominant spongiform encephalopathy: does the infectious agent originate in the human genome?常染色体显性海绵状脑病的实验性传播：感染因子源自人类基因组吗？

Br Med J (Clin Res Ed). 1985 Aug 3;291(6491):299-302. doi: 10.1136/bmj.291.6491.299.

Genetic control of nucleation and polymerization of host precursors to infectious amyloids in the transmissible amyloidoses of brain.在脑的可传播淀粉样变性病中，宿主前体向感染性淀粉样蛋白成核和聚合的遗传控制。

Br Med Bull. 1993 Oct;49(4):913-31. doi: 10.1093/oxfordjournals.bmb.a072653.

Familial cerebral amyloidosis and spongiform encephalopathy.家族性脑淀粉样变性和海绵状脑病。

J Neurol Neurosurg Psychiatry. 1982 Jan;45(1):37-45. doi: 10.1136/jnnp.45.1.37.

引用本文的文献

Identification of a second bovine amyloidotic spongiform encephalopathy: molecular similarities with sporadic Creutzfeldt-Jakob disease.第二种牛淀粉样海绵状脑病的鉴定：与散发性克雅氏病的分子相似性。

Proc Natl Acad Sci U S A. 2004 Mar 2;101(9):3065-70. doi: 10.1073/pnas.0305777101. Epub 2004 Feb 17.

Mechanism of inhibition of Psi+ prion determinant propagation by a mutation of the N-terminus of the yeast Sup35 protein.酵母 Sup35 蛋白 N 端突变抑制 Psi+ 朊病毒决定簇传播的机制。

EMBO J. 1998 Oct 1;17(19):5805-10. doi: 10.1093/emboj/17.19.5805.

Scrapie.

Mol Biotechnol. 1998 Jun;9(3):225-34. doi: 10.1007/BF02915795.

Prion-inducing domain 2-114 of yeast Sup35 protein transforms in vitro into amyloid-like filaments.酵母 Sup35 蛋白的朊病毒诱导结构域 2 - 114 在体外转化为淀粉样细丝。

Proc Natl Acad Sci U S A. 1997 Jun 24;94(13):6618-22. doi: 10.1073/pnas.94.13.6618.

Generation of monoclonal antibodies against human prion proteins in PrP0/0 mice.在PrP0/0小鼠中产生抗人朊病毒蛋白的单克隆抗体。

Mol Med. 1996 Nov;2(6):725-34.

18F-fluorodeoxyglucose-PET and 99mTc-bicisate-SPECT in Creutzfeldt-Jakob disease.18F-氟脱氧葡萄糖-PET和99mTc-比西酯-SPECT在克雅氏病中的应用

Ann Nucl Med. 1996 Feb;10(1):131-4. doi: 10.1007/BF03165066.

Propagation of the yeast prion-like [psi+] determinant is mediated by oligomerization of the SUP35-encoded polypeptide chain release factor.酵母朊病毒样[psi+]决定簇的传播是由SUP35编码的多肽链释放因子的寡聚化介导的。

EMBO J. 1996 Jun 17;15(12):3127-34.

Fibrils in brain of Rocky Mountain elk with chronic wasting disease contain scrapie amyloid.患有慢性消耗病的落基山麋鹿大脑中的纤维含有羊瘙痒病淀粉样蛋白。

Acta Neuropathol. 1993;86(1):77-80. doi: 10.1007/BF00454902.

Microglia is a component of the prion protein amyloid plaque in the Gerstmann-Sträussler-Scheinker syndrome.在格斯特曼-施特劳斯勒-谢inker综合征中，小胶质细胞是朊蛋白淀粉样斑块的一个组成部分。

Acta Neuropathol. 1993;85(6):623-7. doi: 10.1007/BF00334672.

A kinetic model for amyloid formation in the prion diseases: importance of seeding.朊病毒疾病中淀粉样蛋白形成的动力学模型：种子的重要性。

Proc Natl Acad Sci U S A. 1993 Jul 1;90(13):5959-63. doi: 10.1073/pnas.90.13.5959.

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The new biology of spongiform encephalopathy: infectious amyloidoses with a genetic twist.

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