[肝脏恶性横纹肌样瘤伴自发性破裂：1例报告]

[Malignant rhabdoid tumor of the liver with spontaneous rupture: a case report].

作者信息

Clairotte Anne, Ringenbach Frédéric, Laithier Véronique, Aubert Didier, Kantelip Bernadette

机构信息

Service d'Anatomie Pathologique, Hôpital J. Minjoz, boulevard Fleming, 25030 Besançon.

出版信息

Ann Pathol. 2006 Apr;26(2):122-5. doi: 10.1016/s0242-6498(06)70691-5.

DOI:10.1016/s0242-6498(06)70691-5

PMID:16791124

Abstract

We report the case of an 8-year-old child, presenting a rhabdoid tumor of the liver with spontaneous rupture, revealed by an intra-abdominal bleeding with rapidly fatal course. This clinical and pathological report raises the problem of the differential diagnosis of primary malignant hepatic tumors of the child with no alpha-foetoprotein increase.

摘要

我们报告了一例8岁儿童病例，该患儿患有肝脏横纹肌肉瘤且发生自发性破裂，因腹腔内出血而被发现，病情进展迅速，最终致命。这份临床和病理报告提出了一个问题，即对于甲胎蛋白不升高的儿童原发性恶性肝肿瘤，该如何进行鉴别诊断。