Dysfibrinogenemia (fibrinogen Wilmington) due to a novel Aalpha chain truncation causing decreased plasma expression and impaired fibrin polymerisation.

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作者信息

Brennan Stephen O, Mosesson Michael W, Lowen Robin, Frantz Christopher

机构信息

Canterbury Health Laboratories, Christchurch Hospital, Cnr Hagley Ave & Tuam St., Christchurch, New Zealand.

出版信息

Thromb Haemost. 2006 Jul;96(1):88-9. doi: 10.1160/TH05-11-0749.

DOI:10.1160/TH05-11-0749

PMID:16807657

Abstract

摘要

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