• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利：CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法，用中文像聊天一样搜索，搜遍4000万医学文献。AI智能推荐，让科研检索更轻松。

立即免费搜索

文件翻译

保留排版，准确专业，支持PDF/Word/PPT等文件格式，支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述，25分钟生成高质量综述，智能提取关键信息，辅助科研写作。

立即免费体验

Peripheral nerve involvement in Batten-Spielmeyer-Vogt's disease.

作者信息

Lyon B B

出版信息

J Neurol Neurosurg Psychiatry. 1975 Feb;38(2):175-9. doi: 10.1136/jnnp.38.2.175.

DOI:10.1136/jnnp.38.2.175
PMID:168315
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC491882/
Abstract

Electromyography and sensory and motor nerve conduction were studied in 23 patients with Batten-Spielmeyer-Vogt's disease ("juvenile amaurotic idiocy", cerebral ceroidlipofuscinosis). A slight to moderate slowing of the sensory conduction velocity was found in the median as well as in the sural nerve, more pronounced in the distal than in the proximal segments. The findings are interpreted as evidence of impaired transmission of the peripheral nerves in Batten-Spielmeyer-Vogt's disease.

摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8fd3/491882/f885e35caa82/jnnpsyc00176-0074-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8fd3/491882/79d6653350ab/jnnpsyc00176-0073-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8fd3/491882/f885e35caa82/jnnpsyc00176-0074-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8fd3/491882/79d6653350ab/jnnpsyc00176-0073-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8fd3/491882/f885e35caa82/jnnpsyc00176-0074-a.jpg

相似文献

1
Peripheral nerve involvement in Batten-Spielmeyer-Vogt's disease.
J Neurol Neurosurg Psychiatry. 1975 Feb;38(2):175-9. doi: 10.1136/jnnp.38.2.175.
2
[Changes in the peripheral nerves in chronic renal failure].
Pol Arch Med Wewn. 1986 Feb;75(2):116-26.
3
[Changes in the neural conduction in spinal muscular atrophy of the Kennedy type].[肯尼迪型脊髓性肌萎缩症中神经传导的变化]
Neurol Neurochir Pol. 1989 Jul-Dec;23(4-6):283-6.
4
[Hereditary sensorimotor neuropathy in electrophysiological studies].[电生理研究中的遗传性感觉运动神经病]
Neurol Neurochir Pol. 1998 Mar-Apr;32(2):295-308.
5
Transmission of frequent impulse series in sensory nerves of patients with alcoholic polyneuropathy.酒精性多发性神经病患者感觉神经中频繁冲动序列的传导
Eur Neurol. 1974;12(5-6):317-30. doi: 10.1159/000114629.
6
Sensory conduction of the sural nerve in polyneuropathy.腓肠神经在多发性神经病中的感觉传导
J Neurol Neurosurg Psychiatry. 1974 Jun;37(6):647-52. doi: 10.1136/jnnp.37.6.647.
7
Nerve conduction velocity of small components in human sensory nerves. Studies in normal and diseased nerves.人类感觉神经中小成分的神经传导速度。对正常神经和病变神经的研究。
Eur Neurol. 1977;16(1-6):270-9. doi: 10.1159/000114908.
8
Sensory action potentials and biopsy of the sural nerve in neuropathy.神经病中感觉动作电位及腓肠神经活检
Brain. 1978 Sep;101(3):473-93. doi: 10.1093/brain/101.3.473.
9
Conduction of electrically elicited impulses in peripheral nerves of diabetic patients.糖尿病患者外周神经中电诱发冲动的传导
Eur Neurol. 1980;19(1):20-9. doi: 10.1159/000115123.
10
Involvement of the peripheral sensory nervous system in human chronic Chagas disease.
Medicina (B Aires). 1986;46(6):662-8.

引用本文的文献

1
Top-down and bottom-up propagation of disease in the neuronal ceroid lipofuscinoses.神经元蜡样脂褐质沉积症中疾病的自上而下和自下而上传播。
Front Neurol. 2022 Nov 11;13:1061363. doi: 10.3389/fneur.2022.1061363. eCollection 2022.
2
Spielmeyer-Vogt disease: clinical and neurophysiological aspects.
Childs Nerv Syst. 1991 Aug;7(4):226-30. doi: 10.1007/BF00249401.
3
Ultrastructural investigations of peripheral nerves in neuronal ceroid-lipofuscinoses (NCL).神经元蜡样脂褐质沉积症（NCL）中周围神经的超微结构研究。

本文引用的文献

1
Peripheral nerve changes in Tay-Sachs and Batten-Spielmeyer-Vogt disease.泰-萨克斯病和巴顿-施皮勒迈尔-沃格特病中的周围神经变化。
Acta Pathol Microbiol Scand. 1967;70(4):630-2. doi: 10.1111/j.1699-0463.1967.tb01331.x.
2
Low noise alternating current amplifier and compensator to reduce stimulus artefact.低噪声交流放大器和补偿器，用于减少刺激伪迹。
Med Biol Eng. 1970 Sep;8(5):501-8. doi: 10.1007/BF02477187.
3
Normal sensory conduction in the nerves of the leg in man.人类腿部神经的正常感觉传导。
J Neurol. 1976 Oct 4;213(4):295-303. doi: 10.1007/BF00316269.
J Neurol Neurosurg Psychiatry. 1971 Aug;34(4):404-14. doi: 10.1136/jnnp.34.4.404.
4
Electrophysiological findings in entrapment of the median nerve at wrist and elbow.腕部和肘部正中神经卡压的电生理表现
J Neurol Neurosurg Psychiatry. 1974 Mar;37(3):340-60. doi: 10.1136/jnnp.37.3.340.
5
Studies in batten disease. I. Peroxidase deficiency in granulocytes.巴顿病研究。I. 粒细胞中的过氧化物酶缺乏症。
Arch Neurol. 1974 Feb;30(2):144-52. doi: 10.1001/archneur.1974.00490320032004.
6
Peripheral nerve function in long-term therapy with diphenylhydantoin. A clinical and electrophysiologic correlation.苯妥英长期治疗中的周围神经功能。临床与电生理相关性
Neurology. 1974 May;24(5):411-7. doi: 10.1212/wnl.24.5.411.
7
Cytoplasmic inclusions in the vermiform appendix and skeletal muscle in two types of so-called neuronal ceroid-lipofuscinosis.
Brain. 1973 Dec;96(4):833-40. doi: 10.1093/brain/96.4.833.
8
Involvement of sural nerve in neuronal ceroid-lipofuscinoses: report of two cases.腓肠神经受累于神经元蜡样脂褐质沉积症：两例报告。
Neuropadiatrie. 1973 Jan;4(1):98-110. doi: 10.1055/s-0028-1091731.
9
Specific involvement of muscle, nerve, and skin in late infantile and juvenile amaurotic idiocy.肌肉、神经和皮肤在晚期婴儿型和少年型黑蒙性白痴中的特异性受累情况。
Neurology. 1972 Feb;22(2):170-86. doi: 10.1212/wnl.22.2.170.