Duquia Rodrigo Pereira, de Almeida Hiram Larangeira, Traesel Moacir, Jannke Heitor Alberto
Catholic University of Pôrto Alegre, Brazil.
J Am Acad Dermatol. 2006 Aug;55(2):341-4. doi: 10.1016/j.jaad.2005.11.1080.
Pheochromocytoma is a rare tumor originating from neuroectodermic cells. Only 10% of these tumors are malignant. There are many familial forms of this tumor, including multiple endocrine neoplasia type II, Von Hippel-Lindau syndrome, and neurofibromatosis type I. Skin manifestations of pheochromocytoma are rare, and cutaneous metastasis in patients with multiple endocrine neoplasia IIB has never been described. The case of a patient with multiple endocrine neoplasia IIB who presented malignant pheochromocytoma with multiple cutaneous metastasis is described.
嗜铬细胞瘤是一种起源于神经外胚层细胞的罕见肿瘤。这些肿瘤中只有10%是恶性的。这种肿瘤有许多家族性类型,包括II型多发性内分泌肿瘤、冯·希佩尔-林道综合征和I型神经纤维瘤病。嗜铬细胞瘤的皮肤表现罕见,IIB型多发性内分泌肿瘤患者的皮肤转移从未被描述过。本文描述了一例IIB型多发性内分泌肿瘤患者出现恶性嗜铬细胞瘤伴多发皮肤转移的病例。