Alsoufi Bahaaldin, Slater Matthew, Smith Pamela P, Karamlou Tara, Mansoor Atiya, Ravichandran Pasala
Department of Cardiothoracic Surgery, Oregon Health & Sciences University, Portland, USA.
Asian Cardiovasc Thorac Ann. 2006 Aug;14(4):e71-3. doi: 10.1177/021849230601400424.
Intimal sarcomas of the pulmonary artery are rare tumors that are often difficult to distinguish from pulmonary thromboembolic disease, complicating accurate diagnosis and timely therapy. We report the case of a gentleman with a primary pulmonary artery sarcoma who presented with a massive pulmonary embolism and complete right ventricular outflow tract obstruction. The patient's condition was successfully managed with urgent pulmonary artery thromboendarterectomy, pulmonary valve replacement, and tricuspid valve annuloplasty.
肺动脉内膜肉瘤是罕见肿瘤，常难以与肺血栓栓塞性疾病相鉴别，这使得准确诊断和及时治疗变得复杂。我们报告一例原发性肺动脉肉瘤患者，该患者表现为大面积肺栓塞和完全性右心室流出道梗阻。通过紧急肺动脉血栓内膜剥脱术、肺动脉瓣置换术和三尖瓣环成形术，成功治疗了该患者的病情。
