Burgess Scott, Harris Margaret, Dakin Carolyn, Borzi Peter, Ryan Christopher, Cooper David
Department of Respiratory and Sleep Medicine, Mater Children's Hospital, South Brisbane, Australia.
J Paediatr Child Health. 2006 Sep;42(9):560-2. doi: 10.1111/j.1440-1754.2006.00924.x.
A 7-month old infant presented with an effusion and multiple lesions in his spleen. A diagnosis of lymphangiomatosis was made based on chylous effusion and an MRI demonstrating numerous enhancing lesions within the spleen on T2-weighed images. Conservative measures, including the withdrawal of feeds and octreotide, did not significantly reduce the rate of chyle production and increasing requirement for respiratory support. Resection of the patient's spleen and partial pleurectomy were associated with a dramatic improvement in his condition. At 27 months the patient was well with no evidence of further lymphangiomas or a recurrence of his chylothoraces.
一名7个月大的婴儿出现了胸腔积液和脾脏多处病变。基于乳糜性胸腔积液以及磁共振成像（MRI）显示在T2加权图像上脾脏内有大量强化病变，做出了淋巴管瘤病的诊断。包括停止喂食和使用奥曲肽在内的保守措施，并未显著降低乳糜生成率，也未减少对呼吸支持的需求。切除患者的脾脏并进行部分胸膜切除术，使其病情得到了显著改善。在27个月时，患者情况良好，没有进一步的淋巴管瘤迹象或乳糜胸复发。
