Bozić Ivo, Fabijanić Damir, Carević Vedran, Polić Stojan
Division of Cardiology, Split University Hospital, Spincićeva 1, 21000 Split, Croatia.
J Clin Ultrasound. 2006 Oct;34(8):416-21. doi: 10.1002/jcu.20247.
Isolated left ventricular noncompaction (IVNC) is a congenital cardiomyopathy characterized by a loosened spongy myocardium. Recognition of this condition is extremely important because of its high mortality and morbidity due to progressive heart failure, thromboembolic events, and ventricular arrhythmias. However, IVNC is commonly misdiagnosed because of the lack of knowledge about this rare disorder. We report 2 patients with the characteristic echocardiographic presentation for IVNC. Echocardiography is the procedure of choice to confirm the diagnosis and perform follow-up in patients with IVNC; therefore, it is important to make echocardiographers more familiar with this condition.
孤立性左心室心肌致密化不全（IVNC）是一种先天性心肌病，其特征为心肌海绵状结构疏松。认识这种疾病极为重要，因为其因进行性心力衰竭、血栓栓塞事件和室性心律失常导致的高死亡率和高发病率。然而，由于对这种罕见疾病缺乏了解，IVNC常被误诊。我们报告了2例具有IVNC特征性超声心动图表现的患者。超声心动图是确诊IVNC患者并进行随访的首选检查方法；因此，让超声心动图检查人员更熟悉这种疾病很重要。
