无小肠闭锁的背侧肠系膜发育不全：儿童中肠扭转的罕见原因。

Dorsal mesenteric agenesis without small bowel atresia: a rare cause of midgut volvulus in children.

作者信息

Cascio Salvatore, Tien Alan Sze Loong, Agarwal Prakash, Tan Hock Lim

机构信息

Department of Paediatric Surgery, and The University of Adelaide Women's and Children's Hospital, North Adelaide, 5006 Australia.

出版信息

J Pediatr Surg. 2006 Sep;41(9):E5-7. doi: 10.1016/j.jpedsurg.2006.05.011.

DOI:10.1016/j.jpedsurg.2006.05.011

PMID:16952580

Abstract

Agenesis of the dorsal mesentery in association with jejunal atresia is a well-recognized congenital anomaly. Only few reports exist in the English literature of children with agenesis of the dorsal mesentery without small bowel atresia. Herein, we report a child with total mesenteric agenesis presenting with midgut volvulus owing to internal herniation of the small bowel through a mesenteric defect, with normal fixation and rotation of the bowel.

摘要

背侧肠系膜缺如合并空肠闭锁是一种公认的先天性异常。英文文献中仅有少数关于无小肠闭锁的背侧肠系膜缺如患儿的报道。在此，我们报告一例全肠系膜缺如的患儿，其因小肠通过肠系膜缺损发生内疝而出现中肠扭转，肠管固定和旋转正常。