先天性肠系膜缺损中小肠无狭窄的苹果皮样畸形。

Apple peel deformity of the small bowel without atresia in a congenital mesenteric defect.

机构信息

Division of Pediatric Surgery, Department of Surgery, New York University Langone Medical Center, New York, NY 10016, USA.

出版信息

J Pediatr Surg. 2013 Jan;48(1):e9-11. doi: 10.1016/j.jpedsurg.2012.10.009.

DOI:10.1016/j.jpedsurg.2012.10.009

PMID:23331843

Abstract

Congenital mesenteric defects are rare causes of bowel obstruction. Even rarer are mesenteric defects with an apple peel type of deformity, probably described definitively only once previously. We present a case of a 3 year old boy who presented with a septic-like picture of severe metabolic acidosis and lethargy from a bowel obstruction with bowel ischemia. At laparotomy he was found to have bowel infarction due to herniation through a congenital mesenteric defect with an apple peel type of deformity of the bowel without bowel atresia.

摘要

先天性肠系膜缺陷是肠梗阻的罕见原因。更罕见的是具有苹果皮样畸形的肠系膜缺陷，此前可能仅明确描述过一次。我们报告了一例 3 岁男孩的病例，他因肠梗阻伴肠缺血引起严重代谢性酸中毒和昏睡而出现类似脓毒症的表现。剖腹探查时发现他患有肠梗死，原因是肠通过先天性肠系膜缺陷疝出，伴有肠无狭窄的苹果皮样畸形。