Ayres Bernadete, Brasil Oswaldo M, Klejnberg Celso, Moura Letícia R, Fernandes Bruno F, Burnier Miguel N
Instituto Brasileiro de Oftalmologia, Rio de Janeiro, Brazil.
Clin Exp Ophthalmol. 2006 Sep-Oct;34(7):695-8. doi: 10.1111/j.1442-9071.2006.01321.x.
A 3-year-old girl presented with a distorted pupil and decrease of visual acuity. A ciliary body mass at the superior-temporal quadrant could be seen at slit-lamp examination. Ultrasound biomicroscopy revealed a lesion with lobulated surface, arising at the ciliary body, composed of compact and cystic areas. An iridocyclectomy was performed but the tumour recurred after a few months. The eye was then enucleated. Histopathologic evaluation showed sheets and cords of proliferated medullary epithelium. Cystic spaces and Flexner-Wintersteiner rosettes were also seen. Those findings correlated well with ultrasound biomicroscopic images. The knowledge of echographic characteristics can significantly assist in the diagnosis of medulloepithelioma of the ciliary body.
