Ocular Oncology Services, LV Prasad Eye Institute, Hyderabad, India.
Surv Ophthalmol. 2013 May-Jun;58(3):266-72. doi: 10.1016/j.survophthal.2012.08.006. Epub 2012 Dec 6.
A 67-year-old woman presented with complaints of poor vision and persistent redness in the right eye of 4 months duration. She had undergone an uncomplicated cataract surgery in the same eye 2 years ago and had regained visual acuity of 20/20 with a then otherwise unremarkable eye examination. She had only light perception in the affected right eye with an intraocular pressure of 42 mm Hg. There were dilated episcleral vessels inferotemporally. Powdery white material was dispersed over the corneal endothelium and in the anterior chamber. There was diffuse iris neovascularization and a large yellowish white, fluffy, ciliary body mass. A metastasis was suspected, but systemic evaluation failed to reveal a primary. In view of the neovascular glaucoma, poor visual potential, and suspicion of a malignancy, the eye was enucleated. Histopathological examination revealed malignant nonteratoid ciliary body medulloepithelioma. Although ciliary body medulloepithelioma is predominantly a pediatric tumor, this case emphasizes the need to include it in the differential diagnosis of ciliary body tumors in adults.
一位 67 岁女性因右眼视力差和持续发红 4 个月就诊。她 2 年前在同一只眼接受了一次无并发症的白内障手术，术后视力恢复到 20/20，眼部检查无其他异常。她右眼仅有光感，眼压为 42mmHg。下斜向扩张的球结膜血管。角膜内皮和前房散布着粉状白色物质。弥漫性虹膜新生血管和一个大的黄白色、蓬松的睫状体肿块。怀疑是转移瘤，但全身评估未能发现原发性肿瘤。由于新生血管性青光眼、视力预后差和恶性肿瘤的怀疑，进行了眼球摘除术。组织病理学检查显示恶性非畸胎性睫状体髓上皮瘤。虽然睫状体髓上皮瘤主要是小儿肿瘤，但本例强调需要将其纳入成人睫状体肿瘤的鉴别诊断中。
