Danic Michael J, Applefield Daniel J, Brown Morris
Department of Anesthesiology, Henry Ford Hospital, Detroit, MI 48202-2689, USA.
J Clin Anesth. 2006 Sep;18(6):463-5. doi: 10.1016/j.jclinane.2006.02.009.
Lymphangioleiomyomatosis is a rare restrictive lung disease that is often associated with pneumothorax and prolonged intubation. We report the successful anesthetic management of a patient with lymphangioleiomyomatosis, myasthenia gravis, and idiopathic thrombocytopenic purpura undergoing laparoscopic partial nephrectomy for renal lesions, and discuss anesthetic management strategies for this rare disease process.
淋巴管平滑肌瘤病是一种罕见的限制性肺病,常与气胸和长时间插管相关。我们报告了一例患有淋巴管平滑肌瘤病、重症肌无力和特发性血小板减少性紫癜的患者,在接受腹腔镜下肾部分切除术治疗肾脏病变时的成功麻醉管理,并讨论了针对这种罕见疾病过程的麻醉管理策略。