Wu Jim S, Saluja Sanjay, Garcia-Tsao Guadalupe, Chong Alice, Henderson Katherine J, White Robert I
Department of Diagnostic Radiology, Yale University School of Medicine and Yale-New Haven Hospital, New Haven, CT, USA.
AJR Am J Roentgenol. 2006 Oct;187(4):W399-405. doi: 10.2214/AJR.05.1068.
The purpose of our study was to report the multiphasic CT findings in patients with symptomatic liver involvement by hereditary hemorrhagic telangiectasia (HHT) and to correlate the CT findings with the type of clinical presentation.
Patients with symptomatic HHT liver disease have diffuse hepatic telangiectases, a dilated common hepatic artery, and a high incidence of biliary abnormalities. Multiphasic CT is useful in diagnosing liver involvement due to HHT; however, no strong correlation was seen between CT findings and the clinical subtype of HHT liver disease.
我们研究的目的是报告遗传性出血性毛细血管扩张症(HHT)累及肝脏且有症状患者的多期CT表现,并将CT表现与临床表现类型相关联。
有症状的HHT肝病患者存在弥漫性肝毛细血管扩张、肝总动脉扩张以及胆汁异常的高发生率。多期CT有助于诊断HHT所致的肝脏受累;然而,未发现CT表现与HHT肝病临床亚型之间存在强相关性。