Vaziri Mohammad, Mehrazma Meetra
Department of Thoracic Surgery, Hazrat Rasool Hospital, Iran University of Medical Sciences, Tehran, Iran.
Ann Thorac Surg. 2006 Oct;82(4):1500-1. doi: 10.1016/j.athoracsur.2006.02.010.
A 30-year-old woman with Von Recklinghausen's disease was admitted to our hospital because of sudden onset of dyspnea and syncope. A chest roentgenogram showed a massive right pleural effusion and insertion of an intercostal tube drained 1,600 cc of blood. A computed tomographic chest scan with contrast revealed a hyperdense mass in the right paravertebral area. At thoracotomy, retained clotted hemothorax and continued bleeding from tumor vessels was noted. The apex of the right hemithorax and the tumor location was packed. The pathologic diagnosis was ganglioneuroma and follow-up of the patient for 2 years after re-thoracotomy and removal of the packs revealed no complication and morbidity. We report this case to emphasize the importance of early recognition and prompt surgical intervention in spontaneous hemothorax associated with Von Recklinghausen's disease.
一名患有冯雷克林霍增氏病的30岁女性因突然出现呼吸困难和晕厥入住我院。胸部X线片显示右侧大量胸腔积液，插入肋间引流管引出1600毫升血液。胸部增强计算机断层扫描显示右椎旁区域有一高密度肿块。开胸手术时，发现有残留的凝固性血胸且肿瘤血管持续出血。对右半胸顶部和肿瘤部位进行了填塞。病理诊断为神经节瘤，再次开胸手术并取出填塞物后对患者进行了2年随访，未发现并发症和发病情况。我们报告此病例以强调早期识别和及时手术干预在与冯雷克林霍增氏病相关的自发性血胸中的重要性。
