Casanova D, Boon L-M, Vikkula M
Service de chirurgie plastique, hôpital Nord, chemin des Bourrelly, 13015 Marseille, France.
Ann Chir Plast Esthet. 2006 Aug-Oct;51(4-5):373-87. doi: 10.1016/j.anplas.2006.07.018. Epub 2006 Sep 27.
Venous malformations (VM) are localized defects of blood vessels that are due to vascular dysmorphogenesis. These slow-flow lesions can affect any tissue or organ. Clinically, a cutaneous VM is characterized by a bluish mass that is compressible on palpation. Phleboliths are commonly present. Symptoms depend on location and size. VM are often sporadic and isolated, however, they can be associated with other malformations and be part of a syndrome; Klippel-Trenaunay (capillary-lymphatico-venous malformation with limb hypertrophy) is the most common. Glomuvenous malformation (GVM) is another type of venous anomaly. In contrast to VM, GVM is often painful on palpation and not compressible. Clinical diagnosis of VM is often made in the presence of a bluish cutaneous lesion: however, other lesions can mimick VM. The most frequent anomalies are a blue naevus, a hemorrhagic lymphatic malformation, a sub-cutaneous hemangioma or even the presence of dilated superficial normal veins due to underlying venous stenoses. This chapter will detail the clinical characteristics of venous anomalies and their differential diagnosis.
静脉畸形(VM)是由于血管发育异常导致的局限性血管缺陷。这些低流速病变可累及任何组织或器官。临床上,皮肤VM的特征是蓝色肿块,触诊时可压缩。静脉石通常存在。症状取决于位置和大小。VM通常是散发性和孤立性的,然而,它们可与其他畸形相关并成为综合征的一部分;Klippel-Trenaunay综合征(伴有肢体肥大的毛细血管-淋巴管-静脉畸形)最为常见。球静脉畸形(GVM)是另一种静脉异常类型。与VM不同,GVM触诊时通常疼痛且不可压缩。VM的临床诊断通常在出现蓝色皮肤病变时做出:然而,其他病变可模仿VM。最常见的异常是蓝色痣、出血性淋巴管畸形、皮下血管瘤,甚至由于潜在的静脉狭窄而出现扩张的浅表正常静脉。本章将详细介绍静脉异常的临床特征及其鉴别诊断。