Masci Pier Giorgio, Rossi Francesca, Chiarella Francesco
Unità Operativa di Cardiologia, A.O. Santa Corona, Via XXV Aprile 128, 17027 Pietra Ligure, Italy.
Eur J Echocardiogr. 2008 Jan;9(1):63-4. doi: 10.1016/j.euje.2006.08.014.
Discrete subaortic stenosis (DSS) is likely an acquired cardiac disorder which requires anatomic precursors and a genetic background. DSS occurs usually within the first decade, provoking rapidly progressive left ventricular outflow tract obstruction and secondary aortic regurgitation. DSS has been considered for a long time exclusively a disease of infancy and childhood and few reports and small series have described DSS in adulthood and only two cases are reported in elderly. Our case describes a discrete subaortic membranous ridge in an elderly woman with recent onset of dyspnea.