Lützen Ulf, Engellandt Kay
Klinik für Nuklearmedizin, Universitätsklinikum Schleswig- Holstein, Campus Kiel, Arnold- Heller- Str. 9, 24105 Kiel.
Rontgenpraxis. 2006;56(3):93-7. doi: 10.1016/j.rontge.2006.02.001.
Hemangiopericytomas are rare tumors which arise from the pericytes of Zimmermann. They can occur anywhere, where capillaries can be found. Seldomly this primitive mensenchymal tumors are found intracranially. The current classification of the World Health Organization (WHO) lists the Hemangiopericytomas as entity of its own and they belong to the mesenchymal non-meningoendothelial tumors. These tumors are very aggressive. They have a high rate of local recurrence and also a high propensity for late distant metastases. The case presented, is an example for these special characteristics with late development of distant metastases in spite of no Local recurrence. The treatment of both, the primary tumor as well as the recurrence and the distant metastases is radical surgery. The post-operative radiation therapy improves the local control of the tumor. Within the frame of the oncological follow-up the diagnostic imaging procedures play the most important role.
血管外皮细胞瘤是起源于齐默尔曼周细胞的罕见肿瘤。它们可发生于任何有毛细血管的部位。这种原始间充质肿瘤很少发生于颅内。世界卫生组织（WHO）目前的分类将血管外皮细胞瘤列为独立的肿瘤实体，它们属于间充质非脑膜内皮肿瘤。这些肿瘤具有很强的侵袭性。它们局部复发率高，晚期远处转移倾向也高。所呈现的病例就是这些特殊特征的一个例子，尽管没有局部复发，但仍出现了晚期远处转移。原发性肿瘤以及复发和远处转移的治疗方法都是根治性手术。术后放疗可改善肿瘤的局部控制。在肿瘤学随访过程中，诊断性成像检查起着最重要的作用。
