Cheng Suk Hang, Ng Margaret H L, Lau Kin Mang, Liu Herman S Y, Chan Joyce C W, Hui Angela B Y, Lo Kwok Wai, Jiang Hua, Hou Jian, Chu Raymond W, Wong Wai Shan, Chan Natalie P H, Ng Ho Keung
Department of Anatomical and Cellular Pathology, The Chinese University of Hong Kong, Prince of Wales Hospital, Shatin, New Territories, Hong Kong, China.
Blood. 2007 Mar 1;109(5):2089-99. doi: 10.1182/blood-2006-04-018770. Epub 2006 Oct 31.
In this study, we have elucidated the chromosomal imbalances in the multistep pathogenesis and delineated several critical tumor suppressor gene (TSG) loci in multiple myeloma (MM). By using comparative genomic hybridization, allelotyping, and multicolor interphase fluorescence in situ hybridization, 5 MM cell lines and bone marrow CD138+ plasma cells from 88 Chinese patients with monoclonal gammopathy of undetermined significance (MGUS) and early and advanced stages of MM were investigated. In all MGUS and MM samples, chromosome copy number abnormalities were detected. A higher number of chromosomal imbalances and specific genetic alterations are involved in MGUS to MM transition (-6q, +3p, and +1p) and MM progression (+2p and +9q). In addition to -13q, we first found high frequencies (42% to 46%) of -4q involving high percentages (70% to 74%) of clonal plasma cells in both MGUS and MM, suggesting that inactivation of TSG in this region is also a potentially critical genetic event in MM tumorigenesis. By high-resolution allelotyping, we defined a common deletion region on 4q13.3 and found that a candidate TSG, platelet factor 4, was frequently silenced by promoter hypermethylation in MM (15 of 28) and MM cell lines (5 of 5). These data have opened up a new approach in the molecular targeting therapy and provide novel insights into MM tumorigenesis.
在本研究中,我们阐明了多步骤发病机制中的染色体失衡,并确定了多发性骨髓瘤(MM)中的几个关键肿瘤抑制基因(TSG)位点。通过使用比较基因组杂交、等位基因分型和多色间期荧光原位杂交,对5株MM细胞系以及来自88例中国意义未明的单克隆丙种球蛋白病(MGUS)、MM早期和晚期患者的骨髓CD138 +浆细胞进行了研究。在所有MGUS和MM样本中均检测到染色体拷贝数异常。在MGUS向MM的转变(-6q、+3p和+1p)以及MM进展(+2p和+9q)过程中,涉及更多数量的染色体失衡和特定的基因改变。除了-13q外,我们首次发现-4q的高频缺失(42%至46%),在MGUS和MM中均涉及高比例(70%至74%)的克隆性浆细胞,这表明该区域TSG的失活也是MM肿瘤发生中一个潜在的关键遗传事件。通过高分辨率等位基因分型,我们确定了4q13.3上的一个常见缺失区域,并发现一个候选TSG——血小板因子4,在MM(28例中的15例)和MM细胞系(5株中的5株)中经常因启动子高甲基化而沉默。这些数据为分子靶向治疗开辟了一条新途径,并为MM肿瘤发生提供了新的见解。