儿童肾上腺皮质嗜酸性细胞瘤

Adrenocortical oncocytoma in a child.

作者信息

Gumy-Pause Fabienne, Bongiovanni Massimo, Wildhaber Barbara, Jenkins Jesse J, Chardot Christophe, Ozsahin Hulya

机构信息

Department of Pediatrics, Hematology/Oncology Unit, University Hospital of Geneva, Switzerland.

出版信息

Pediatr Blood Cancer. 2008 Mar;50(3):718-21. doi: 10.1002/pbc.21090.

DOI:10.1002/pbc.21090

PMID:17091483

Abstract

Adrenocortical oncocytoma is a rare epithelial tumor only described in adults. We report the case of a 12-year-old female who presented a left adrenal mass with abdominal pain, fatigue, acne vulgaris, and elevation of the androstenedione and total testosterone. She had an adrenalectomy. A diagnosis of adrenocortical oncocytoma was made after detailed histological, immunohistochemical, and ultrastructural studies.

摘要

肾上腺皮质嗜酸性细胞瘤是一种仅在成人中被描述的罕见上皮性肿瘤。我们报告了一例12岁女性病例，该患者出现左侧肾上腺肿块，并伴有腹痛、乏力、寻常痤疮以及雄烯二酮和总睾酮升高。她接受了肾上腺切除术。经过详细的组织学、免疫组织化学和超微结构研究后，确诊为肾上腺皮质嗜酸性细胞瘤。