Hsiao Hsi-Lin, Wu Wen-Jeng, Chang Mei-Yu, Ke Hung-Lung, Huang Chun-Hsiung
Department of Urology, Kaohsiung Medical University Hospital and Kaohsiung Medical University, Kaohsiung, Taiwan.
Kaohsiung J Med Sci. 2006 Oct;22(10):515-8. doi: 10.1016/S1607-551X(09)70346-8.
Multilocular cystic nephroma is an unusual entity of uncertain etiology that can affect children and adults equally. This lesion is believed to be part of a spectrum of renal cystic disorders with multilocular cyst and cystic Wilms' tumor representing the two extremes and usually presents with a benign character. We report a 22-year-old female who presented with a painful right renal mass and gross hematuria. After a series of examinations including abdominal ultrasound, computed tomography, and angiography, she underwent partial nephrectomy under the impression of benign lesion. The pathologic examination showed that it was a multilocular cystic nephroma. At the 11-month follow-up, the patient was completely asymptomatic and free of recurrence and metastasis.
多房性囊性肾瘤是一种病因不明的罕见疾病，可同等程度地影响儿童和成人。这种病变被认为是肾囊性疾病谱的一部分，多房性囊肿和囊性肾母细胞瘤代表了两个极端，通常表现为良性特征。我们报告一名22岁女性，她出现右侧肾区疼痛性肿块及肉眼血尿。经过包括腹部超声、计算机断层扫描和血管造影在内的一系列检查后，她在被诊断为良性病变的情况下接受了部分肾切除术。病理检查显示为多房性囊性肾瘤。在11个月的随访中，患者完全无症状，无复发和转移。
