Domşa I, Crişan Doiniţa, Olinici C D
Department of Pathology, Railroad Hospital, Cluj-Napoca.
Rom J Morphol Embryol. 2006;47(2):187-91.
Retroperitoneal synovial sarcomas are very rare. The authors describe a 39-year-old male with a primary retroperitoneal synovial sarcoma showing a monophasic pattern. Immunohistochemically, the tumor cells were positive for cytokeratin AE1/AE3, epithelial membrane antigen, vimentin, S-100 protein, CD99 and calretinin. The differential diagnosis, clinical evolution and principles of treatment are shortly discussed.
腹膜后滑膜肉瘤非常罕见。作者描述了一名39岁男性,患有表现为单相型的原发性腹膜后滑膜肉瘤。免疫组织化学检查显示,肿瘤细胞细胞角蛋白AE1/AE3、上皮膜抗原、波形蛋白、S-100蛋白、CD99和钙视网膜蛋白呈阳性。本文简要讨论了鉴别诊断、临床进展及治疗原则。