McCarthy A, Savage K, Gabriel A, Naceur C, Reis-Filho J S, Ashworth A
The Breakthrough Breast Cancer Research Centre, Institute of Cancer Research, London SW3 6JB, UK.
J Pathol. 2007 Mar;211(4):389-98. doi: 10.1002/path.2124.
Breast cancers arising in carriers of germline BRCA1 mutations frequently have a basal-like phenotype. Basal-like cancers are characterized by high histological grade, central necrotic areas, foci with metaplastic differentiation, lack of hormone receptor and HER2 (ErbB2) expression, and consistent positivity for basal markers, including CK5/6, CK14, and EGFR. We have used germline manipulation to generate a conditional mouse model of Brca1 deficiency. Transgenic expression of Cre recombinase in the mammary gland of these mice results in deletion of exons encoding the C-terminus of Brca1 and leads to tumour formation when combined with heterozygosity for a p53 mutation. Histologically, these mammary gland tumours were characterized by high histological grade, central necrotic areas, and presence of homologous metaplastic elements. These metaplastic elements consisted of neoplastic spindle cells or squamous cell differentiation in the form of keratin pearls or individual cell keratinization. Immunohistochemical analysis revealed expression of basal-like markers in all cases. The tumour phenotype generated in our mouse model was compared with published data on human basal-like breast carcinomas and also with metaplastic breast cancers with a basal-like phenotype; the comparison showed that we have generated a mouse model of basal-like breast cancer, which should prove useful in testing new and targeted treatments for this type of breast cancer.
携带种系BRCA1突变的个体所患乳腺癌通常具有基底样表型。基底样癌的特征为组织学分级高、中央坏死区域、伴有化生分化的病灶、缺乏激素受体和HER2(ErbB2)表达,以及基底标志物(包括CK5/6、CK14和EGFR)持续呈阳性。我们利用种系操作构建了Brca1缺陷的条件性小鼠模型。在这些小鼠的乳腺中,Cre重组酶的转基因表达导致编码Brca1 C末端的外显子缺失,当与p53突变的杂合性相结合时会导致肿瘤形成。组织学上,这些乳腺肿瘤的特征为组织学分级高、中央坏死区域以及存在同源化生成分。这些化生成分由肿瘤性梭形细胞或以角化珠或单个细胞角化形式存在的鳞状细胞分化组成。免疫组织化学分析显示所有病例中均有基底样标志物表达。我们将在小鼠模型中产生的肿瘤表型与已发表的关于人类基底样乳腺癌的数据以及具有基底样表型的化生性乳腺癌的数据进行了比较;比较结果表明,我们构建了一个基底样乳腺癌的小鼠模型,这将证明对测试针对这类乳腺癌的新型靶向治疗方法有用。