Tampi Chandralekha, Lotwala Vikram, Lakdawala Muffazal, Coelho Kiran
Department of Pathology, Lilavati Hospital and Research Centre, A-791, Bandra Reclamation, Bandra (West), Mumbai-400 005, India.
Gynecol Oncol. 2007 Apr;105(1):266-8. doi: 10.1016/j.ygyno.2007.01.008. Epub 2007 Feb 15.
Tailgut cyst [retrorectal hamartomas] is an unusual cystic lesion, located in the retrorectal space. It develops from post anal foetal gut remnants, present anterior to the sacrum and posterior to the rectum. A high index of clinical suspicion is required to diagnose this rare tumour. This malformative lesion should be distinguished from teratomas, mullerian cysts, anal gland cysts and duplication cysts of the rectum. The treatment of choice is complete surgical excision.
A tailgut cyst is hereby reported, which had undergone malignant transformation, with development of an adenocarcinoma. Only 16 additional cases of tailgut cysts with adenocarcinoma were recovered, in an extensive search of world literature.
The identification of this rare entity provides an opportunity to examine this pathological rarity in the context of the few previously reported cases of this type.
尾肠囊肿[直肠后错构瘤]是一种位于直肠后间隙的罕见囊性病变。它由胎儿肛门后肠管残余发育而来，位于骶骨前方和直肠后方。诊断这种罕见肿瘤需要高度的临床怀疑。这种发育异常的病变应与畸胎瘤、苗勒管囊肿、肛门腺囊肿和直肠重复囊肿相鉴别。治疗的选择是完整的手术切除。
本文报告一例发生恶性转化并发展为腺癌的尾肠囊肿。在广泛检索世界文献后，仅另外发现16例尾肠囊肿合并腺癌的病例。
识别这种罕见的实体为在少数先前报道的此类病例背景下研究这种病理罕见情况提供了机会。
Zotero 插件