发生于尾肠囊肿的神经内分泌癌。
Neuroendocrine carcinoma arising in a tailgut cyst.
作者信息
Al Khaldi Maher, Mesbah Amanda, Dubé Pierre, Isler Marc, Mitchell Andrew, Doyon Josée, Sideris Lucas
机构信息
Department of Surgery, Division of General Surgical Oncology, Hôpital Maisonneuve-Rosement, University of Montreal, Canada.
Department of Surgery, Division of General Surgical Oncology, Hôpital Maisonneuve-Rosement, University of Montreal, Canada.
出版信息
Int J Surg Case Rep. 2018;49:91-95. doi: 10.1016/j.ijscr.2018.05.032. Epub 2018 Jun 28.
INTRODUCTION
A tailgut cyst, also called retrorectal cystic hamartoma, is a rare congenital lesion that forms most commonly in the retrorectal space. It is presumed to arise from remnants of early embryogenesis.
PRESENTATION OF CASE
The following report describes a unique case of a retrorectal cystic hamartoma in a 53 year-old French Canadian man with a history of low back pain. The tumour underwent malignant transformation into a well-differentiated neuroendocrine carcinoma three years after the beginning of symptoms.
DISCUSSION
This condition can be found at any age, but occurs especially among middle-aged women. Not only is it frequently misdiagnosed, but also several complications associated to the cyst have been reported such as infection and malignant transformation. This is why complete surgical excision of the tailgut cyst is currently recommended.
引言
尾肠囊肿，也称为直肠后囊性错构瘤，是一种罕见的先天性病变，最常见于直肠后间隙。据推测，它起源于早期胚胎发育的残余组织。
病例介绍
以下报告描述了一名53岁法裔加拿大男子的直肠后囊性错构瘤的独特病例，该男子有腰痛病史。症状出现三年后，肿瘤发生恶性转化，变为高分化神经内分泌癌。
讨论
这种疾病可在任何年龄发现，但尤其在中年女性中发生。它不仅经常被误诊，而且还报告了与囊肿相关的几种并发症，如感染和恶性转化。这就是为什么目前建议对尾肠囊肿进行完整的手术切除。
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