da Silva Benedito Borges, Lopes-Costa Pedro Vitor, Furtado-Veloso Ana Maria, Borges Rafael Soares
Department of Gynecology, Federal University of Piauí, Teresina, Piauí, Brazil.
Gynecol Oncol. 2007 May;105(2):539-41. doi: 10.1016/j.ygyno.2007.01.022. Epub 2007 Feb 15.
Epithelioid hemangioendothelioma (EH) is a rare vascular tumor whose localization in the vulva is extremely rare.
The present case report refers to a 19-year-old Brazilian woman admitted to hospital with an extensive lesion of granulomatous appearance on the right labium majus. Following confirmation of the diagnosis of epithelioid hemangioendothelioma, the only treatment consisted of hemivulvectomy and right inguinal lymphadenectomy. Patient was lost to follow-up for 8 years after recovery from surgery. She reappeared 4 years ago and is now being followed-up. There is no sign of recurrence of the disease.
EH is a lesion of unpredictable malignancy whose localization in the vulva is extremely rare. The first therapeutic option is surgical resection.
上皮样血管内皮瘤（EH）是一种罕见的血管肿瘤，其在外阴的定位极为罕见。
本病例报告涉及一名19岁的巴西女性，因右侧大阴唇出现广泛的肉芽肿样病变入院。确诊为上皮样血管内皮瘤后，唯一的治疗方法是半外阴切除术和右侧腹股沟淋巴结切除术。患者术后康复后失访8年。4年前再次出现，目前正在接受随访。没有疾病复发的迹象。
EH是一种恶性程度不可预测的病变，其在外阴的定位极为罕见。首要的治疗选择是手术切除。
