Ciliberti Maria Paola, Caponio Raffaella, Pascali Antonio, Matichecchia Gabriele, Lioce Marco
U.O. Radioterapia - National Cancer Research Centre - Istituto Tumori "Giovanni Paolo II", viale Orazio Flacco, 65-70124, Bari, Italy.
J Med Case Rep. 2015 Apr 29;9:91. doi: 10.1186/s13256-015-0565-0.
Epithelioid hemangioendothelioma (EHE) is a rare endothelial tumor with an intermediate grade of malignancy. Few cases of primary vascular hemangioendothelioma have been described in the literature. Surgery is the treatment of choice, but radiation therapy and chemotherapy should also be considered in particular cases.
We present the case of a 44-year-old Caucasian woman affected by EHE of the cephalic vein, treated by complete surgical removal of the mass and postoperative local radiation therapy. At 5-year follow-up, our patient is alive, with no signs of local or distant relapse and with no late radiation-related effects.
Postoperative radiotherapy may play a role in cases in which tumor margins are close or cannot be assessed or when high-risk features are present.
上皮样血管内皮瘤（EHE）是一种罕见的具有中等恶性程度的内皮肿瘤。文献中描述的原发性血管内皮瘤病例很少。手术是首选治疗方法，但在特定情况下也应考虑放疗和化疗。
我们报告了一例44岁白种女性头静脉上皮样血管内皮瘤的病例，通过完整手术切除肿块及术后局部放疗进行治疗。在5年的随访中，我们的患者存活，无局部或远处复发迹象，也无放疗相关的晚期效应。
在肿瘤切缘接近或无法评估或存在高危特征的情况下，术后放疗可能发挥作用。
