Böge G, Gallix B, Gresillon C, Khau Van Kien A, Veerapen R, Quéré I
Abteilung für Innere Medizin und Gefässkrankheiten, Universitätskrankenhaus Saint Eloi.
Vasa. 2007 Feb;36(1):33-40. doi: 10.1024/0301-1526.36.1.33.
Primary angiosarcoma of the aorta is a rare disease. The prognosis is poor, resulting of embolic complications and early metastatic disease, with a median survival of nine months. Diagnosis is difficult and often made post-mortem. We report the case of a 68-year-old woman referred for a thrombosis of the superior mesenteric artery, occurring a few weeks after resection of an angiosarcoma of the small intestine, disclosing a primary angiosarcoma of the aortic wall with metastatic disease.
原发性主动脉血管肉瘤是一种罕见疾病。其预后较差，原因是栓塞并发症和早期转移性疾病，中位生存期为9个月。诊断困难，且常于尸检时确诊。我们报告一例68岁女性病例，该患者因肠系膜上动脉血栓形成前来就诊，此情况发生在小肠血管肉瘤切除术后几周，结果发现是主动脉壁原发性血管肉瘤伴转移性疾病。
