Peretta Paola, Carlino Christian, Gennari Fabrizio, Ferrero Giovanbattista, Ragazzi Paola, Bradac Gianni Boris, Stura Guido, Cinalli Giuseppe
Department of Pediatric Neurosurgery, "Regina Margherita" Children's Hospital, San Giovanni Battista Hospital, Turin, Italy.
J Neurosurg. 2007 Feb;106(2 Suppl):147-52. doi: 10.3171/ped.2007.106.2.147.
The authors describe the clinical and radiological findings in a case of brainstem arteriovenous malformation (AVM) associated with a hepatic patent ductus venosus (PDV) in a 12-year-old child. The AVM was discovered on magnetic resonance (MR) imaging performed because of slight mental retardation and headache. The malformation was otherwise asymptomatic and no treatment was proposed. An abdominal ultrasonography study performed 1 year later because of hyperammonemia revealed a PDV, which was surgically ligated. One year later, MR images and angiograms showed complete resolution of the brainstem AVM. This report is the first documentation of an association between these two entities in the same patient, and the possible pathophysiological interactions between them are discussed.
作者描述了一名12岁儿童脑干动静脉畸形(AVM)合并肝静脉导管未闭(PDV)的临床和影像学表现。该AVM是在因轻度智力发育迟缓及头痛进行磁共振(MR)成像检查时发现的。该畸形无其他症状,未建议进行治疗。1年后因高氨血症进行的腹部超声检查发现了PDV,并对其进行了手术结扎。1年后,MR图像和血管造影显示脑干AVM完全消退。本报告首次记录了同一患者中这两种病变的关联,并讨论了它们之间可能的病理生理相互作用。