Kurisu A, Kawachi Y, Maruyama H, Kuwabara N
Department of Surgery, Musashino Red-Cross Hospital, Tokyo, Japan.
Dis Colon Rectum. 1992 Jan;35(1):78-81. doi: 10.1007/BF02053344.
A case of tubular colonic duplication, sigmoid colon diverticulum, and lumbar anterior spina bifida in a 28-year-old man was diagnosed as split notochord syndrome. After subtotal colectomy, including the duplicated colon, the patient recovered. Histologic study of the duplicated colon revealed multifocal, ectopic gastric fundic mucosa in a mosaic pattern. Since bleeding and perforation occur most frequently in conjunction with ectopic gastric mucosa within the duplication, we believe that complete resection of the duplicated bowel is the best procedure. Split notochord syndrome is a rare congenital anomaly. It is usually discovered in the first year of life, and the majority of reported cases have involved the cervical or thoracic region. Our patient is exceptional in having reached the age of 28 years without complaints and in that his case involved lumbar anterior spina bifida and tubular colonic duplication.
一名28岁男性患者，患有管状结肠重复畸形、乙状结肠憩室和腰椎前脊柱裂，被诊断为分裂脊索综合征。在进行包括重复结肠在内的结肠次全切除术后，患者康复。对重复结肠的组织学研究显示，有呈镶嵌状的多灶性异位胃底黏膜。由于重复畸形内的异位胃黏膜最常伴发出血和穿孔，我们认为完整切除重复肠段是最佳手术方式。分裂脊索综合征是一种罕见的先天性异常。它通常在出生后第一年被发现，大多数报道的病例累及颈部或胸部区域。我们的患者很特殊，他28岁时仍无任何症状，且其病例涉及腰椎前脊柱裂和管状结肠重复畸形。
