Ma Hui-Jun, Zhao Guang, Liu Wen, Dang Yu-Ping, Li Dong-Guang
Department of Dermatology, The Airforce General Hospital of Chinese People's Liberation Army, 30 Fucheng Road, Haidian District, Beijing 100036, P.R.China.
Eur J Dermatol. 2007 Mar-Apr;17(2):160-3. doi: 10.1684/ejd.2007.0132. Epub 2007 Mar 2.
Unilateral linear capillaritis (ULC) is a rare special variation of pigmented purpuric dermatosis (PPD), which is characterized clinically by linear or segmental distribution of pigmented purpuric macules located predominantly on the lower extremities and showing a favorable prognosis. In this case report, we describe two unusual cases of ULC, in one male and one female patient, with unilateral lesions involving the upper extremities that loosely follow the dermatome lines. Biopsy results revealed a common histopathology feature to PPD without heavy band-like infiltration in the upper dermis. On review 20 months after the onset, the eruptions of Patient 1 had spontaneously faded from parts of the affected area. Meanwhile, after a period of 18 months post onset, the eruptions of Patient 2 had became less visible after treatment with PUVA for 2 months, leaving a faded pigmentation.
单侧线状毛细血管炎(ULC)是色素性紫癜性皮病(PPD)一种罕见的特殊类型,其临床特征为主要位于下肢的色素性紫癜性斑疹呈线状或节段性分布,预后良好。在本病例报告中,我们描述了两例不寻常的ULC病例,分别为一名男性患者和一名女性患者,其单侧病变累及上肢,大致沿皮节线分布。活检结果显示具有PPD的常见组织病理学特征,真皮上层无重度带状浸润。发病20个月后复查,患者1病变部位部分皮疹已自行消退。同时,发病18个月后,患者2经2个月的补骨脂素加长波紫外线(PUVA)治疗后皮疹消退,仅留淡色素沉着。