一名3岁男孩患Mauriac综合征。
Mauriac syndrome in a 3-year-old boy.
作者信息
Mahesh Shefali, Karp Robert J, Castells Salvador, Quintos Jose Bernardo Q
机构信息
Department of Pediatric Nephrology, Montefiore Medical Center, Bronx, New York, USA.
出版信息
Endocr Pract. 2007 Jan-Feb;13(1):63-6. doi: 10.4158/EP.13.1.63.
OBJECTIVE
To report a case of Mauriac syndrome in a young child with poorly controlled type 1 diabetes mellitus.
METHODS
We describe the typical features of Mauriac syndrome and review the clinical, laboratory, and ultrasound findings and follow-up results in our current patient.
RESULTS
Hepatomegaly, growth impairment, and cushingoid features characterize Mauriac syndrome. Most frequently, it is seen in adolescents and young adults with a history of poor glycemic control. In our current patient, a 3-year-old boy with type 1 diabetes mellitus of 2 years' duration, Mauriac syndrome developed in the context of a disrupted social environment. His liver enzyme derangement, hepatomegaly, and growth improved once euglycemia was achieved.
CONCLUSION
Although Mauriac syndrome is currently uncommon, close monitoring of children with type 1 diabetes is important to maintain optimal glycemic control and prevent such an occurrence.
目的
报告1例1型糖尿病控制不佳的幼儿患Mauriac综合征的病例。
方法
我们描述了Mauriac综合征的典型特征，并回顾了当前患者的临床、实验室及超声检查结果和随访结果。
结果
肝肿大、生长发育障碍和库欣样特征是Mauriac综合征的特点。该综合征最常见于有血糖控制不佳病史的青少年和青年。在我们当前的患者中，一名患1型糖尿病2年的3岁男孩，在社会环境紊乱的情况下患上了Mauriac综合征。一旦实现血糖正常，他的肝酶紊乱、肝肿大和生长发育情况均有改善。
结论
尽管Mauriac综合征目前并不常见，但密切监测1型糖尿病患儿对于维持最佳血糖控制和预防此类情况的发生很重要。
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